Source Code Name Case count Share of cases (%)
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M353) Polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 4146
OUTPAT OUTPAT_ICD10(M353) Polymyalgia rheumatica 3841
OUTPAT OUTPAT_ICD10(M350) Sicca syndrome [Sjögren] 2847
INPAT INPAT_ICD10(M353) Polymyalgia rheumatica 2020
OUTPAT OUTPAT_ICD10(M357) Hypermobility syndrome 1725
OUTPAT OUTPAT_ICD10(M359) Systemic involvement of connective tissue, unspecified 1621
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M350) Sicca syndrome [Sjögren]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 1428
OUTPAT OUTPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 1029
OUTPAT OUTPAT_ICD10(M329) Systemic lupus erythematosus, unspecified 956
INPAT INPAT_ICD10(M350) Sicca syndrome [Sjögren] 894
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M357) Hypermobility syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 621
INPAT INPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 606
OUTPAT OUTPAT_ICD10(M351) Other overlap syndromes 581
INPAT INPAT_ICD10(M329) Systemic lupus erythematosus, unspecified 481
OUTPAT OUTPAT_ICD10(M313) Wegener's granulomatosis 480
OUTPAT OUTPAT_ICD10(M341) CR(E)ST syndrome 473
INPAT INPAT_ICD10(M359) Systemic involvement of connective tissue, unspecified 419
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M329) Systemic lupus erythematosus, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 370
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 366
INPAT INPAT_ICD10(M357) Hypermobility syndrome 338
INPAT INPAT_ICD10(M313) Wegener's granulomatosis 336
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M359) Systemic involvement of connective tissue, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 326
OUTPAT OUTPAT_ICD10(M349) Systemic sclerosis, unspecified 316
OUTPAT OUTPAT_ICD10(M321) Systemic lupus erythematosus with organ or system involvement 272
OUTPAT OUTPAT_ICD10(M328) Other forms of systemic lupus erythematosus 257
OUTPAT OUTPAT_ICD10(M332) Polymyositis 229
OUTPAT OUTPAT_ICD10(M316) Other giant cell arteritis 219
OUTPAT OUTPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 210
INPAT INPAT_ICD10(M351) Other overlap syndromes 201
OUTPAT OUTPAT_ICD10(M320) Drug-induced systemic lupus erythematosus 197
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M341) CR(E)ST syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 191
OUTPAT OUTPAT_ICD10(M358) Other specified systemic involvement of connective tissue 184
INPAT INPAT_ICD10(M321) Systemic lupus erythematosus with organ or system involvement 173
INPAT INPAT_ICD9(7100A) Systemic lupus erythematosus 173
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M313) Wegener's granulomatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 169
OUTPAT OUTPAT_ICD10(M355) Multifocal fibrosclerosis 167
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M351) Other overlap syndromes. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 165
OUTPAT OUTPAT_ICD10(M317) Microscopic polyangiitis 163
INPAT INPAT_ICD10(M341) CR(E)ST syndrome 155
OUTPAT OUTPAT_ICD10(M311) Thrombotic microangiopathy 152
OUTPAT OUTPAT_ICD10(M339) Dermatopolymyositis, unspecified 150
OUTPAT OUTPAT_ICD10(M331) Other dermatomyositis 139
OUTPAT OUTPAT_ICD10(M300) Polyarteritis nodosa 138
INPAT INPAT_ICD10(M332) Polymyositis 131
INPAT INPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 129
OUTPAT OUTPAT_ICD10(M340) Progressive systemic sclerosis 129
OUTPAT OUTPAT_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss] 114
OUTPAT OUTPAT_ICD10(M310) Hypersensitivity angiitis 114
INPAT INPAT_ICD10(M316) Other giant cell arteritis 113
OUTPAT OUTPAT_ICD10(M318) Other specified necrotizing vasculopathies 110
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M32) Systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 107
INPAT INPAT_ICD9(7250A) Polymyalgia rheumatica 106
INPAT INPAT_ICD10(M300) Polyarteritis nodosa 102
INPAT INPAT_ICD10(M349) Systemic sclerosis, unspecified 100
INPAT INPAT_ICD10(M311) Thrombotic microangiopathy 96
INPAT INPAT_ICD10(M317) Microscopic polyangiitis 96
INPAT INPAT_ICD10(M328) Other forms of systemic lupus erythematosus 96
OUTPAT OUTPAT_ICD10(M348) Other forms of systemic sclerosis 92
OUTPAT OUTPAT_ICD10(M352) Behçet's disease 91
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M349) Systemic sclerosis, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 91
INPAT INPAT_ICD9(7102B) Diffuse diseases of connective tissue, Sicca syndrome 87
INPAT INPAT_ICD10(M339) Dermatopolymyositis, unspecified 86
INPAT INPAT_ICD8(73491) Diffuse diseases of connective tissue, Collagenosis NUD 83
INPAT INPAT_ICD9(7109X) Unspecified diffuse connective tissue disease 80
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M316) Other giant cell arteritis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 79
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M332) Polymyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 78
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M328) Other forms of systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 73
INPAT INPAT_ICD10(M310) Hypersensitivity angiitis 72
INPAT INPAT_ICD10(M320) Drug-induced systemic lupus erythematosus 66
INPAT INPAT_ICD9(7102A) Diffuse diseases of connective tissue, Sicca syndrome 64
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M35) Other systemic involvement of connective tissue. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 64
OUTPAT OUTPAT_ICD10(M308) Other conditions related to polyarteritis nodosa 62
INPAT INPAT_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss] 61
INPAT INPAT_ICD10(M331) Other dermatomyositis 61
INPAT INPAT_ICD10(M318) Other specified necrotizing vasculopathies 59
OUTPAT OUTPAT_ICD10(M32) Systemic lupus erythematosus 58
INPAT INPAT_ICD9(4476A) Arteritis, unspecified 55
OUTPAT OUTPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 55
INPAT INPAT_ICD10(M340) Progressive systemic sclerosis 54
INPAT INPAT_ICD10(M355) Multifocal fibrosclerosis 53
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M321) Systemic lupus erythematosus with organ or system involvement. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 50
INPAT INPAT_ICD10(M308) Other conditions related to polyarteritis nodosa 49
INPAT INPAT_ICD10(M348) Other forms of systemic sclerosis 44
OUTPAT OUTPAT_ICD10(M354) Diffuse (eosinophilic) fasciitis 43
OUTPAT OUTPAT_ICD10(M303) Mucocutaneous lymph node syndrome [Kawasaki] 42
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M339) Dermatopolymyositis, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 42
INPAT INPAT_ICD10(M358) Other specified systemic involvement of connective tissue 41
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M358) Other specified systemic involvement of connective tissue. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 41
INPAT INPAT_ICD10(M303) Mucocutaneous lymph node syndrome [Kawasaki] 39
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M34) Systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 38
OUTPAT OUTPAT_ICD10(M330) Juvenile dermatomyositis 37
OUTPAT OUTPAT_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere 36
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M317) Microscopic polyangiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 33
INPAT INPAT_ICD10(M352) Behçet's disease 32
INPAT INPAT_ICD9(7108X) Other specified diffuse diseases of connective tissue 32
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M319) Necrotizing vasculopathy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 32
DEATH DEATH_ICD10(M353) Polymyalgia rheumatica 31
INPAT INPAT_ICD8(44698) Polyarteritis nodosa and allied conditions, Other 31
INPAT INPAT_ICD8(73490) Diffuse diseases of connective tissue, Keratoconjunctivitis sicca (dry eye disease). Sjögren's syndrome 31
INPAT INPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 30
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M331) Other dermatomyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 29
DEATH DEATH_ICD10(M313) Wegener's granulomatosis 28
INPAT INPAT_ICD9(4461A) Acute febrile mucocutaneous lymph node syndrome [MCLS] 28
INPAT INPAT_ICD9(4462A) Hypersensitivity angiitis 28
OUTPAT OUTPAT_ICD10(M35) Other systemic involvement of connective tissue 27
OUTPAT OUTPAT_ICD10(M368) Systemic disorders of connective tissue in other diseases classified elsewhere 27
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 27
INPAT INPAT_ICD9(4465A) Giant cell arteritis 26
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M300) Polyarteritis nodosa. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 25
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M348) Other forms of systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 25
OUTPAT OUTPAT_ICD10(M362) Haemophilic arthropathy (D66-D68+) 24
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M352) Behçet's disease. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 24
INPAT INPAT_ICD9(4464A) Wegener's granulomatosis 23
INPAT INPAT_ICD8(73498) Diffuse diseases of connective tissue, Alii definiti 22
INPAT INPAT_ICD9(7101A) Diffuse diseases of connective tissue, Systemic sclerosis 22
INPAT INPAT_ICD10(M330) Juvenile dermatomyositis 21
INPAT INPAT_ICD9(7104A) Polymyositis 20
INPAT INPAT_ICD8(71610) Polymyositis and dermatomyositis, Polymyositis 19
INPAT INPAT_ICD8(73499) Diffuse diseases of connective tissue, Other and unspecified 19
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M340) Progressive systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 19
INPAT INPAT_ICD10(M354) Diffuse (eosinophilic) fasciitis 18
INPAT INPAT_ICD8(44638) Polyarteritis nodosa and allied conditions, Polymyalgia arteritica (rheumatica) 18
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M314) Aortic arch syndrome [Takayasu]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 18
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M355) Multifocal fibrosclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 18
INPAT INPAT_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere 17
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M354) Diffuse (eosinophilic) fasciitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 17
OUTPAT OUTPAT_ICD10(M312) Lethal midline granuloma 15
DEATH DEATH_ICD10(M341) CR(E)ST syndrome 14
DEATH DEATH_ICD10(M350) Sicca syndrome [Sjögren] 14
INPAT INPAT_ICD8(71600) Polymyositis and dermatomyositis, Dermatomyositis 14
INPAT INPAT_ICD9(4460A) Polyarteritis nodosa and allied conditions, Polyarteritis nodosa 14
OUTPAT OUTPAT_ICD10(M361) Arthropathy in neoplastic disease (C00-D48+) 14
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M310) Hypersensitivity angiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 14
DEATH DEATH_ICD10(M329) Systemic lupus erythematosus, unspecified 13
DEATH DEATH_ICD10(M332) Polymyositis 13
INPAT INPAT_ICD9(7103B) Diffuse diseases of connective tissue, Dermatomyositis 13
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M318) Other specified necrotizing vasculopathies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 13
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 13
INPAT INPAT_ICD10(M362) Haemophilic arthropathy (D66-D68+) 12
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M30) Polyarteritis nodosa and related conditions. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 12
DEATH DEATH_ICD10(M317) Microscopic polyangiitis 11
DEATH DEATH_ICD10(M359) Systemic involvement of connective tissue, unspecified 11
INPAT INPAT_ICD8(73409) Diffuse diseases of connective tissue, Sclerosis systematica NUD 11
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M308) Other conditions related to polyarteritis nodosa. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 11
INPAT INPAT_ICD10(M368) Systemic disorders of connective tissue in other diseases classified elsewhere 10
OUTPAT OUTPAT_ICD10(M356) Relapsing panniculitis [Weber-Christian] 10
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M311) Thrombotic microangiopathy. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 10
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M33) Dermatopolymyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 10
INPAT INPAT_ICD10(M361) Arthropathy in neoplastic disease (C00-D48+) 9
INPAT INPAT_ICD8(44600) Polyarteritis nodosa and allied conditions, Polyarteritis nodosa 9
INPAT INPAT_ICD8(44630) Polyarteritis nodosa and allied conditions, Arteritis cranialis (temporalis) 9
OUTPAT OUTPAT_ICD10(M34) Systemic sclerosis 9
INPAT INPAT_ICD9(4466A) Thrombotic microangiopathy 8
INPAT INPAT_ICD9(7103A) Diffuse diseases of connective tissue, Dermatomyositis 8
INPAT INPAT_ICD8(73401) Diffuse diseases of connective tissue, Sclerosis systematica acrosclerotica 7
INPAT INPAT_ICD8(74310) Other congenital anomalies of nervous system, Microcephalus 7
INPAT INPAT_ICD9(4467A) Takayasu's disease 7
OUTPAT OUTPAT_ICD10(M342) Systemic sclerosis induced by drugs and chemicals 7
OUTPAT OUTPAT_ICD10(M360) Dermato(poly)myositis in neoplastic disease (C00-D48+) 7
DEATH DEATH_ICD10(M300) Polyarteritis nodosa 6
DEATH DEATH_ICD10(M331) Other dermatomyositis 6
INPAT INPAT_ICD10(M312) Lethal midline granuloma 6
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M320) Drug-induced systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 6
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M330) Juvenile dermatomyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 6
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M362) Haemophilic arthropathy (D66-D68+). Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 6
DEATH DEATH_ICD10(M311) Thrombotic microangiopathy 5
DEATH DEATH_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 5
DEATH DEATH_ICD10(M319) Necrotizing vasculopathy, unspecified 5
DEATH DEATH_ICD10(M349) Systemic sclerosis, unspecified 5
DEATH DEATH_ICD10(M351) Other overlap syndromes 5
INPAT INPAT_ICD8(44620) Polyarteritis nodosa and allied conditions, Other hypersensitivity angiitis 5
INPAT INPAT_ICD9(4460B) Polyarteritis nodosa and allied conditions, Polyarteritis nodosa 5